Diagnoslista/länkar

Listor över diagnoser som expertteamet ansvarar för.

Familial Electrical Diseases/ Familjära elektriska sjukdomar?

Svenska namn på diagnoserna?

  • Long QT syndrome -  Lång QT syndrom (LQTS)
  • Short QT syndrome - Kort QT syndrom
  • Brugada syndrome – Brugada syndrom (BS)
  • Catecholaminergic polymorphic ventricular tachycardia –
  • Katekolaminerg polymorf ventrikeltakykardi (CPVT)
  • Idiopathic ventricular fibrillation – Idiopatisk ventrikulär fibrillation

Familial Cardiomyopathies / Familjär kardiomyopati?

Svenska namn?

  • Arrhythmogenic cardiomyopathy – arytmogenisk kardiomyopati.

  • Dilated cardiomyopathy – Dilaterad kardiomyopati (DCM)

  • Hypertrophic cardiomyopathy – Hypertrof kardiomyopati (HCM)

  • Restrictive cardiomyopathy

  • Non-compaction cardiomyopathy

  • Arytmogen högerkammarkardiomyopati (ARVC)


Special Electrophysiology Conditions/ Särskilda elektrofysiologiska tillstånd?

Vilka diagnoser (svenska namn)?

Cardiac ablations are performed at a frequent basis in adult population and old children. These procedures are performed at a much lower frequency in small children. Nowadays, cardiac ablations are considered a first-line treatment for those patients with tachycardiomyopathy and for incessant tachycardias refractory to several drugs. Eventhough, numbers are low, and expertise is difficult to be reached, thus these procedures are performed in only few centers in order to be held safely for the patient. Expertise in minimal procedure and radiation times and minimal catheter usage ensures better results.